Resection of a Late Retroperitoneal Metastatic Leydig–Sertoli Cell Sex Cord–Stromal Tumor With Concomitant Aortocaval Reconstruction

Leydig–Sertoli cell tumors are rare, with only a few cases reported in the literature. We here present a 41-year-old man who underwent a right orchiectomy for a testicular tumor at the age of 34 years. Seven years later, he presented at our institution with a large retroperitoneal mass encasing the abdominal great vessels. The patient underwent en bloc resection of the mass and concomitant infrarenal aorta, and inferior vena cava reconstruction. Pathology report revealed a Leydig–Sertoli cell sex cord–stromal tumor. The patient recovered well from the surgery and was discharged home in stable condition. To our knowledge this is the first report of a Leydig–Sertoli cell sex cord–stromal tumor with late retroperitoneal metastasis treated by en bloc resection and vascular reconstruction of the abdominal great vessels.