Open AccessA Intresting Case of Struge Weber Syndrome
Author(s) -
Vikram B Vikhe,
Prakash Shende,
Harish Choudhari,
Ridhima Jakotia
Publication year - 2022
Publication title -
journal of pharmaceutical research international
Language(s) - English
Resource type - Journals
ISSN - 2456-9119
DOI - 10.9734/jpri/2022/v34i19b35814
Subject(s) - hemiparesis , medicine , atrophy , sturge–weber syndrome , pediatrics , epilepsy , calcification , radiology , surgery , pathology , psychiatry , angiography
Struge Weber Syndrome is a rare neurocutaneous disorder characterized by Leptomeninigeal & facial angiomas mainly in the course of ophthalmic& maxillary branches of the trigeminal nerve. We report a case of 14 year old male who presented with left hemiparesis since 2 to 3months & Generalized tonic clonic seizures since 5days.Diagnosis is confirmed by CT/MRI. The classical findings seen on CT/MRI are atrophy and calcification of the cerebral hemisphere. The most common neurological symptom seen are seizures, they are typically focal tonic clonic seizures, seen during first year of life. They are often refractory to anti-convulsants. Most children present with slowly progressive hemiparesis during the course of illness.