Open AccessUnguarded Tricuspid Orifice with Congenitally Corrected Transposition of the Great Arteries and Aortic Atresia- A Highly Unusual Case
Author(s) -
Carolin Puegge,
I. Altmann,
Michael Weidenbach
Publication year - 2021
Publication title -
cardiology and angiology: an international journal
Language(s) - English
Resource type - Journals
ISSN - 2347-520X
DOI - 10.9734/ca/2021/v10i430181
Subject(s) - great arteries , pulmonary atresia , regurgitation (circulation) , medicine , cardiology , tricuspid atresia , tricuspid valve , ventricular outflow tract , atresia , pulmonary artery , surgery , heart disease
Unguarded tricuspid orifice is a very rare anomaly. It is characterised by the absence of one or more of the tricuspid valve leaflets resulting in severe tricuspid regurgitation and right heart failure. It is rarely an isolated anomaly but more often associated with pulmonary atresia and intact ventricular septum. When the ventricles are inverted however, the result of outflow tract obliteration is not pulmonary atresia, but aortic atresia. This anomaly has been described in the literature in only 2 cases so far. We present a case of a neonate with unguarded tricuspid orifice with absence of all tricuspid leaflets, congenitally corrected transposition of the great arteries and aortic atresia. The severe tricuspid regurgitation and right ventricular enlargement would have required a Norwood-like procedure combined with a right ventricular plication. Due to the complexity of this lesion no surgical therapy was attempted in consent with the parents.