Open AccessPrimary Pulmonary Primitive Neuro- Ectodermal Tumour (PNET) in an Eight- Year-Old Girl - Report of a Rare Case
Author(s) -
Radhika Narayan,
J Sreedevi,
Farah Rana,
Meenakshi Mishra,
Rajesh Mohanty
Publication year - 2016
Publication title -
journal of clinical and diagnostic research
Language(s) - English
Resource type - Journals
eISSN - 2249-782X
pISSN - 0973-709X
DOI - 10.7860/jcdr/2016/19709.8839
Subject(s) - girl , medicine , primitive neuroectodermal tumor , pathology , sarcoma , biology , genetics
Primitive Neuro-Ectodermal-Tumours (PNET) and Ewing's sarcoma are part of the spectrum of Ewing's Family of Tumours (EFT) and show varying degrees of neuroectodermal differentiation. Both these tumours share similar histological and genetic features. PNETs arising primarily in the lungs without pleural or chest wall involvement are extremely rare. We report a case of pulmonary PNET in an eight-year-old girl. To the best of our knowledge, this is the youngest case of primary pulmonary PNET to be reported in paediatric age group in the Indian literature.