Open AccessDermatofibrosarcoma Protuberans – A Recurrent Lesion with Unusual Presentation in the Parotid Region
Author(s) -
Usha Hegde,
Sujeeth Kumar Shetty,
HS Sreeshyla,
Vidya Doddawada
Publication year - 2014
Publication title -
journal of clinical and diagnostic research
Language(s) - English
Resource type - Journals
eISSN - 2249-782X
pISSN - 0973-709X
DOI - 10.7860/jcdr/2014/7068.4133
Subject(s) - dermatofibrosarcoma protuberans , medicine , cd34 , lesion , distant metastasis , presentation (obstetrics) , head and neck , metastasis , dermatology , pathology , surgery , biology , cancer , genetics , stem cell
Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous malignant neoplasm consisting of relatively monomorphous mononuclear spindle cells that show diffuse CD34+ positivity. Management of this lesion poses problem because of its infiltrative margins and high propensity for local recurrence and rare distant metastasis. It is said that clear margins with minimal removal of normal tissues can be achieved by Mohs' micrographic surgery, which is particularly important in head and neck locations where the presence of vital anatomical structures and aesthetic considerations hinders a wide surgical excision. A case of DFSP, at a very uncommon site of parotid region, which recurred within 9 months after initial surgical treatment, is being reported.