
Behavior of Blood Pressure Variables in Children and Adolescents with Duchenne Muscular Dystrophy
Author(s) -
Fabiane R. R. H. Marui,
Henrique Tria Bianco,
Maria Teresa Nogueira Bombig,
Natascha G. F. Palmeira,
José Marcos Thalenberg,
Fernando Focaccia Póvoa,
Maria Cristina de Oliveira Izar,
Francisco Antônio Helfenstein Fonseca,
Acary Sb Oliveira,
Rms Póvoa
Publication year - 2018
Publication title -
arquivos brasileiros de cardiologia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.4
H-Index - 53
eISSN - 1678-4170
pISSN - 0066-782X
DOI - 10.5935/abc.20180085
Subject(s) - medicine , blood pressure , ambulatory blood pressure , duchenne muscular dystrophy , cardiology , left ventricular hypertrophy , pediatrics
Duchenne muscular dystrophy is an X-chromosome-linked genetic disorder (locus Xp21). Involvement of the cardiovascular system is characterized by fibrous degeneration/replacement of myocytes with consequent ventricular hypertrophy and arterial hypertension.