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Dwustronny pierwotny pigmentowany rozrost drobnoguzkowy nadnerczy jako składnik zespołu Carney — opis przypadku
Author(s) -
Dorota Sikorska,
Lucyna Papierska,
Ewa Mojs,
Ewa Makowska,
Marek Ruchała,
Włodzimierz Samborski
Publication year - 2017
Publication title -
endokrynologia polska
Language(s) - Uncategorized
Resource type - Journals
SCImago Journal Rank - 0.413
H-Index - 27
eISSN - 2299-8306
pISSN - 0423-104X
DOI - 10.5603/ep.2017.0008
Subject(s) - medicine , carney complex , myxoma , pathology , dermatology , gynecology , biochemistry , gene , chemistry
We report a case of a 20-year-old patient with Cushing's syndrome as a component of Carney syndrome. Carney syndrome is an autosomal dominant disease with co-existing bilateral pigmented nodular adrenal disease, heart and skin myxoma, skin pigmentation, breast fibroadenoma, testicular and ovarian tumours, thyroid tumours, and pituitary adenomas. (Endokrynol Pol 2017; 68 (1): 70-72).

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