Open AccessNadir bir hastalık; spontan pnömotoraks ile başvuran Erdheim-Chester hastalığı
Author(s) -
Mustafa Buğra Coşkuner,
Tevfik Özlü,
Yılmaz Bülbül
Publication year - 2019
Publication title -
tuberkuloz ve toraks/tüberküloz ve toraks
Language(s) - Turkish
Resource type - Journals
SCImago Journal Rank - 0.157
H-Index - 18
ISSN - 0494-1373
DOI - 10.5578/tt.68541
Subject(s) - erdheim–chester disease , histiocyte , histiocytosis , medicine , cd68 , pathology , etiology , infiltration (hvac) , disease , immunohistochemistry , physics , thermodynamics
Erdheim-Chester disease (ECD) is a rare non-Langerhans histiocytosis of unknown etiology, it is characterized by organ infiltration of foamy histiocytes. Diagnosis of ECD involves the analysis of histiocytes in tissue biopsies: these are typically CD68+ CD1a-. These characteristic histiocytes may be found in almost any tissue in cases of ECD. We present an interesting case of ECD that was presented by spontaneous pneumothorax and neurological involvement.