
Tratamiento de las malformaciones en extremidades en el síndrome de bridas amnióticas: a propósito de un caso
Author(s) -
Enrique Guillén Botaya,
L. Pino Almero,
María O Molini Menchón,
Virina González Alonso,
Manuel Pérez-Montejano,
María Fe Mínguez Rey
Publication year - 2020
Publication title -
archivos argentinos de pediatría
Language(s) - Spanish
Resource type - Journals
eISSN - 1668-3501
pISSN - 0325-0075
DOI - 10.5546/aap.2020.e486
Subject(s) - amniotic band syndrome , medicine , amniotic band , syndactyly , clubfoot , fetus , tenotomy , surgery , gynecology , pregnancy , tendon , deformity , biology , genetics
Amniotic band syndrome consists in a group of congenital abnormalities caused by strands of the amniotic sac that entangle some parts of the fetus. Those strands result from premature rupture of amnios. The incidence of amniotic band syndrome is 1:1200 to 1:15,000 live births, depending on case studies. Mostly affected parts of fetus are limbs (asymmetric amputations, syndactyly and clubbed foot) but facial and thoracoabdominal abnormalities have also been described. Recent works have proved the utility of Ponseti method to treat clubfoot associated with amniotic band syndrome. We report the case of a newborn with amniotic band syndrome focusing on management and surgical repair of limbs deformities. Especially, we highlight the use of Ponseti method in treatment of syndromic clubfoot.