
Fístula broncobiliar congénita. Caso clínico
Author(s) -
Cinthia Giselle Pérez,
Aixa Reusmann
Publication year - 2016
Publication title -
archivos argentinos de pediatría
Language(s) - Uncategorized
Resource type - Journals
SCImago Journal Rank - 0.236
H-Index - 19
eISSN - 1668-3501
pISSN - 0325-0075
DOI - 10.5546/aap.2016.e350
Subject(s) - medicine , fistula , anastomosis , left main bronchus , surgery , intubation , biliary fistula , bronchoscopy
Congenital tracheo-or-bronchobiliary fistula or congenital he-patopulmonary fistula is a rare malformation with high morbidity and mortality if the diagnosis is not made early. The tracheo-or-bronchobiliary fistula is a communication between the respiratory (trachea or bronchus) and biliary tract. To date, only 35 cases have been published worldwide. We report a case of a neonate with right pneumonia and bilious fluid in the endotracheal tube. Diagnosis was made using bronchoscopy with fluoroscopy. Videothoracoscopy was used to remove the bronchobiliary fistula. Subsequently, a left he-patectomy with Roux-en-Y biliary-digestive anastomosis was performed as bile ductus hypoplasia was present.