
Enfermedad de Rosai-Dorfman. A propósito de un caso
Author(s) -
Silvia Adriana Maffía,
María V. Peruffo,
Roque Malvaso,
Varinea Senor,
Daniel Pollono,
Eugenia Altamirano
Publication year - 2015
Publication title -
archivos argentinos de pediatría
Language(s) - Spanish
Resource type - Journals
SCImago Journal Rank - 0.236
H-Index - 19
eISSN - 1668-3501
pISSN - 0325-0075
DOI - 10.5546/aap.2015.e327
Subject(s) - medicine , etiology , rosai–dorfman disease , sinus histiocytosis with massive lymphadenopathy , histiocytosis , cervical lymphadenopathy , lymph , cervical lymph nodes , dermatology , disease , pathology , cancer , metastasis
Rosai-Dorfman disease, also known as sinus histiocytosis with massive lymphadenopathy, is a rare dis order of unknown etiology, generally associated with enlargement of superficial and/or deep lymph nodes. Most patients do not require treatment. We report the case of a 10 month old infant who was admitted with a left cervical tumor of 25 days duration.