Open AccessLOW-GRADE FIBROMYXOID SARCOMA ADJACENT TO NEURAL STRUCTURE IN A 3 YEAR OLD GIRL: CASE REPORT AND REVIEW OF LITERATURE
Author(s) -
Salih Onur Başat,
Turgut Kayadibi,
İsmail Mithat Akan,
Mehmet Fatih Bozkurt
Publication year - 2014
Publication title -
el ve mikrocerrahi
Language(s) - English
Resource type - Journals
ISSN - 2146-1155
DOI - 10.5455/handmicrosurg.167837
Subject(s) - sarcoma , medicine , girl , soft tissue , soft tissue sarcoma , pathology , dermatology , biology , genetics
Low-grade fibromyxoid sarcoma (LGFMS) is a rare adult mesenchymal tumor located mostly in deep soft tissues, which is not common in the pediatric patients. Only 20% of reported cases show patients under the age of 18. A systematic literature review of articles between 1995 and 2013 in MEDLINE and PubMed shows that fewer than 10 fibromyxoid sarcoma have thus far been identified in childhood. In this report authors describe a case of low-grade fibromyxoid sarcoma in the right arm of a 3-year-old girl. The tumor was excised with preservation of nearby neural structures, there was no functional deficit in arm functions and in follow-ups no recurrences have been seen so far. To the best of our knowledge, this is the youngest case of low-grade fibromyxoid sarcoma. [Hand Microsurg 2014; 3(1.000): 20-23