Susac syndrome. Case report.

Context: Susac Syndrome, was first described in 1979, by neurologist John Susac, and is characterized by a clinical triad consisting of: central nervous system dysfunction, visual changes and sensorineural hearing loss. Although the pathophysiology is not yet fully understood, the description occurs with microangiopathy involving arteries of the brain, retina and cochlea. The manifestation of the clinical triad has a monophasic and self-limiting course.This case report was approved by the Ethics Committee of Universidade Metropolitana de Santos. Case Report: The present case refers to a female patient, 40 years old, caucasian, and presented a sudden decrease in the visual acuity of the left eye, with visual blurring and dyschromatopsia. After 3 days, he sought medical assistance from an ophthalmologist, already presenting amaurosis of his left eye. Occlusion of distal branches of the retinal artery of the left eye was confirmed. He had a personal history of recurrent major depression and obsessive-compulsive disorder with sub-optimal response to drug treatment. Evaluated with neurology, referring to a decrease in asymmetric auditory acuity. Bilateral sensorineural hearing loss confirmed. Skull MRI was performed and showed multiple images of central lesions in the corpus callosum (“snow ball lesions”), as well as lesions in the white matter of the brain. Conclusions: The diagnosis of Susac syndrome was established and symptomatic treatment was performed, presenting with clinical stabilization.