Open AccessEfficacy of Living Donor Liver Transplantation in Patients with Methylmalonic Acidemia
Author(s) -
Jae Guk Jang,
Seak Hee Oh,
Yu Bin Kim,
Seo Hee Kim,
HanWook Yoo,
Beom Hee Lee,
JungMan Namgoong,
Dae Yeon Kim,
KiHun Kim,
GiWon Song,
DeokBog Moon,
Shin Hwang,
SungGyu Lee,
Kyung Mo Kim
Publication year - 2021
Publication title -
pediatric gastroenterology, hepatology and nutrition
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.44
H-Index - 19
eISSN - 2234-8646
pISSN - 2234-8840
DOI - 10.5223/pghn.2021.24.3.288
Subject(s) - medicine , methylmalonic acidemia , liver transplantation , transplantation , hemodialysis , gastroenterology , incidence (geometry) , surgery , physics , optics
Despite aggressive medical and nutritional management, patients with methylmalonic acidemia (MMA) often suffer from multi-organ damage. Early deceased donor liver transplantation (DDLT) has emerged as an intervention to prevent disease progression. We investigated the efficacy of living donor LT (LDLT) with a potential carrier of MMA and a small volume of graft in patients with MMA as an alternative to DDLT.