Open AccessLUNG LYMPHANGIOLEIOMYOMATOSIS
Author(s) -
В. А. Штанзе,
В. Н. Бондаренко,
D. Yu. Ruzanov,
V. A. Anufriev,
S. A. Smolitskiy,
Т. Т. Шебушева
Publication year - 2016
Publication title -
problemy zdorovʹâ i èkologii
Language(s) - English
Resource type - Journals
eISSN - 2708-6011
pISSN - 2220-0967
DOI - 10.51523/2708-6011.2016-13-3-21
Subject(s) - lymphangioleiomyomatosis , pathology , lung , lymphatic system , medicine , etiology , tuberous sclerosis
Lymphangioleiomyomatosis is a rare interstitial lung disease of unknown etiology which is characterized by progressive diffuse infiltrating growth of neoplastic smooth muscle-like cells, cystic lung destruction, and obliteration of lymphatic and blood vessels