Open AccessCochlear Implantation in Congenital Long-QT Syndrome: A Comprehensive Study
Author(s) -
Ronald Anto,
S. Sudha Maheswari,
Senthil Vadivu,
Mohan Kameswaran
Publication year - 2019
Publication title -
the journal of international advanced otology/the journal of international advanced otology
Language(s) - Uncategorized
Resource type - Journals
SCImago Journal Rank - 0.518
H-Index - 13
eISSN - 2148-3817
pISSN - 1308-7649
DOI - 10.5152/iao.2019.7404
Subject(s) - medicine , cochlear implantation , qt interval , long qt syndrome , referral , cochlear implant , pediatrics , surgery , anesthesia , audiology , family medicine
Jervell and Lange-Nielsen syndrome is a rare autosomal recessive disease characterized by congenital sensorineural deafness and significant QT interval prolongation. Aims were to study the prevalence of long QT in congenital hearing loss, complications encountered, outcomes by Categories of auditory Performance (CAP) scores and Speech Intelligibility Rating (SIR) scores and to create an algorithm with precautions to be followed in Long QT children.