Open AccessCaroli’s Disease: A Mini-Review
Author(s) -
J McCafferty,
Li C
Publication year - 2022
Publication title -
japanese journal of gastroenterology and hepatology
Language(s) - English
Resource type - Journals
ISSN - 2435-1210
DOI - 10.47829/jjgh.2022.8401
Subject(s) - medicine , disease , congenital hepatic fibrosis , intrahepatic bile ducts , modalities , gastroenterology , bile duct , general surgery , radiology , portal hypertension , cirrhosis , social science , sociology
Caroli’s disease is a rare congenital condition that is characterised by intrahepatic biliary duct dilatation without fibrosis. It is associated with an increased risk of cholelithiasis, cholangitis and cholangiocarcinoma. As such, it is an important clinical entity to be aware of. Most of the literature surrounding Caroli’s disease is limited to case reports and case series. This review will explore the clinical characteristics, imaging modalities and management of Caroli’s disease