Open AccessExtra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation
Author(s) -
Jaishri Ramji,
Rakesh S. Joshi,
Mitesh Bachani,
Dungarsingh Rathore
Publication year - 2013
Publication title -
journal of neonatal surgery
Language(s) - English
Resource type - Journals
ISSN - 2226-0439
DOI - 10.47338/jns.v2.56
Subject(s) - medicine , biliary atresia , polysplenia , sepsis , atresia , jaundice , gastroenterology , intestinal malrotation , intestinal atresia , liver transplantation , transplantation , situs inversus
The syndromic form of biliary atresia accounts for 10-25% and is associated with a poor prognosis due to associated anomalies. We report a case of extrahepatic biliary atresia and polysplenia syndrome with jaundice since 19th day of life and who had undergone surgical correction of malrotation in the neonatal period. Inspite of successful Kasai’s portoenterostomy at 52nd day of life, the child succumbed to post-operative sepsis.