Open AccessMckusick-Kaufman Syndrome Presenting as Acute Intestinal Obstruction
Author(s) -
Ramesh B Hatti,
Ashok V Badakali,
R N Vanaki,
VijayMahantesh S Samalad
Publication year - 2013
Publication title -
journal of neonatal surgery
Language(s) - English
Resource type - Journals
ISSN - 2226-0439
DOI - 10.47338/jns.v2.19
Subject(s) - medicine , polydactyly , intestinal malrotation , surgery , anatomy
Hydrometrocolpos and polydactyly have been associated with many syndromes and can present at any age. Rarely does hydrometrocolpos present as neonatal intestinal obstruction. We report two cases of McKusick-Kaufman syndrome presenting with intestinal obstruction. In both cases, intestinal obstruction got relieved after a cutaneous vaginostomy.