
Large Gastric Perforation in Carmi Syndrome: A Morbid Complication in a Rare Association
Author(s) -
Manoj Joshi,
L Krishnan,
S Kuruvila
Publication year - 2012
Publication title -
journal of neonatal surgery
Language(s) - English
Resource type - Journals
ISSN - 2226-0439
DOI - 10.47338/jns.v1.8
Subject(s) - medicine , complication , perforation , epidermolysis bullosa , surgery , peritonitis , pediatrics , dermatology , materials science , punching , metallurgy
The association between epidermolysis bullosa (EB) and congenital pyloric atresia (CPA) named Carmi Syndrome is rare. We report unusual and morbid complication of gastric perforation resulting in peritonitis in a preterm neonate born with Carmi Syndrome.