Open AccessInterstitial Pneumonia with Autoimmune Features (IPAF): Case Report
Author(s) -
María Victoria Lobo,
María Cecilia Goizueta
Publication year - 2021
Publication title -
revista argentina de reumatología
Language(s) - English
Resource type - Journals
eISSN - 2362-3675
pISSN - 0327-4411
DOI - 10.47196/rar.v32i1.369
Subject(s) - medicine , ctd , context (archaeology) , multidisciplinary approach , presentation (obstetrics) , intensive care medicine , surgery , geography , archaeology , social science , oceanography , sociology , geology
IPAF groups individuals with ILD and other clinical, serologic, or pulmonary manifestations with an underlying systemic autoimmune condition, but do not meet current rheumatologic criteria for a CTD. ILD is a frequent clinical manifestation of CTDs; may appear in the context of a well known CTD but is often the first and only manifestation of an unknown CTD. Identifying an underlying CTD in patients presenting with initial interstitial involvement can be challenging; such evaluations can be optimized using a multidisciplinary approach. We present the case of three patients, of different presentation, evolution and treatment, all characterized to date as IPAF.