Vulvar Sikatrisyel Pemfigoid: Bir Çocuk Olgu

Summary\udVulvar cicatricial pemphigoid is a rare variant of bullous pemphigoid, which is characterized by isolated and localized vulvar involvement observed in childhood. The typical clinical finding is the vulvar erosive lesions healing with scar formation. Ocular involvement may be associated with the vulvar disease or may develop during the follow-up. On histopathologic examination of the lesions, subepidermal blister and on direct immunofluorescence study linear deposition of Ig G and C3 are observed. In the differential diagnosis, lichen sclerosus and sexual abuse are the primary diseases which should be considered at first. Topical and systemic steroids and dapson are the main treatment options. Ophthalmological examination and follow up should be repeated on every six months for ocular involvement. Here, we report development of vulvar cicatricial pemphigoid in a 11-year-old girl with clinical and histopathological findings