Open AccessClassical Triad in Pulmonary Arteriovenous Malformation: Clubbing, Cyanosis and Policytemia
Author(s) -
Hikmet Tekin Nacaroğlu,
Saniye Gülle,
Özlem Bağ,
Hüdaver Alper,
Mustafa Bak,
Demet Can
Publication year - 2013
Publication title -
güncel pediatri
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.126
H-Index - 4
eISSN - 1308-6308
pISSN - 1304-9054
DOI - 10.4274/jcp.11.08208
Subject(s) - medicine , triad (sociology) , arteriovenous malformation , cardiology , radiology , psychology , psychoanalysis
Pulmonary arteriovenous malformations (PAVM) are generally congenital lesions that results from an abnormal capillary development. Lesions can be presented as an isolated single anomaly, or may be multiple when accompanying with autosomal dominant hereditary hemorrhagic telangiectasia (Rendu-Osler-Weber Syndrome; ROWS). These cases may be asymptomatic, but exertional dyspnea, palpitations and easy fatigability may also be seen. The classic radiological appearance is a round, well-circumscribed lesions. Computed tomography of thorax and angiography are also useful for diagnosis. Herein, we present 2 and 13 years old girls with the diagnosis of PAVM with clubbing and cyanosis. (Journal of Current Pediatrics 2013;11:92-5