Open AccessSuperior mesenteric artery syndrome in a patient with Charcot Marie Tooth disease
Author(s) -
Óscar Dario Gómez Beltrán,
Ana Belén Martínez,
María del Carmen Pérez Manrique,
Joaquín Sánchez Rodríguez,
Enrique Lizárraga Febres,
Sebastián Rufían Peña
Publication year - 2011
Publication title -
world journal of gastrointestinal surgery
Language(s) - English
Resource type - Journals
ISSN - 1948-9366
DOI - 10.4240/wjgs.v3.i12.197
Subject(s) - medicine , superior mesenteric artery syndrome , abdominal distension , vomiting , surgery , abdominal pain , distension , epigastric pain , superior mesenteric artery , anesthesia
The extrinsic compression of the third part of the duodenum as it passes through the aorto-mesenteric angle is known as the superior mesenteric artery syndrome (SMAS). This syndrome is a rare mechanical cause of upper intestinal obstruction, with a reported incidence of between 0.2% and 0.78%. Clinical manifestations of SMAS may be chronic or acute; chronic symptoms include intermittent gastric pain, fullness and occasional episodes of postprandial vomiting, while acute symptoms include incoercible vomiting, oral intolerance, mainly epigastric abdominal distension and abdominal pain. Surgery is recommended only when initial conservative treatment fails. Here, we report what appears to be the third published case of SMAS associated with hereditary motor and sensory neuropathy or Charcot Marie Tooth disease.