Open AccessA fatal case of Degos’ disease which presented with recurrent intestinal perforation
Author(s) -
Mona Ahmadi,
Sevil Agabalaey Rafi,
Zhale Faham,
Ramin Azhough,
Samad Beheshty Rooy,
Omid Rahmani
Publication year - 2011
Publication title -
world journal of gastrointestinal surgery
Language(s) - English
Resource type - Journals
ISSN - 1948-9366
DOI - 10.4240/wjgs.v3.i10.156
Subject(s) - medicine , perforation , etiology , peritonitis , disease , surgery , gastrointestinal tract , dermatology , gastroenterology , materials science , punching , metallurgy
Degos' disease, otherwise known as "malignant atrophic papulosis" is a rare vasculopathy with an unknown etiology characterized by typical cutaneous lesions. Involvement of the gastrointestinal (GI) tract is observed in approximately half of patients and small infarctions in the mucosa can cause perforation and resulting peritonitis, the leading cause of death. We present a fatal case of Degos' disease with skin and GI involvement, manifesting as recurrent intestinal perforations and peritonitis, in a 15-year-old Iranian boy.