Open AccessDoege-Potter syndrome by malignant solitary fibrous tumor of the liver: A case report and review of literature
Author(s) -
Antonella Delvecchio,
Loren Duda,
Maria Conticchio,
Felicia Fiore,
Stefano Lafranceschina,
Umberto Riccelli,
Antonella Cristofano,
Bianca Pascazio,
Anna Colagrande,
Leonardo Resta,
Riccardo Méméo
Publication year - 2019
Publication title -
world journal of gastrointestinal surgery
Language(s) - English
Resource type - Journals
ISSN - 1948-9366
DOI - 10.4240/wjgs.v11.i8.348
Subject(s) - medicine , surgery , hepatectomy , radiology , resection
Solitary fibrous tumor of the liver (SFTL) is a rare occurrence with a low number of cases reported in literature. SFTL is usually benign but, 10%-20% cases are reported to be malignant with a tendency to metastasize. The majority of malignant SFTL cases are associated with a paraneoplastic hypoglycaemia defined as Doege-Potter syndrome. Surgery is the best therapeutic treatment, however, long- life follow-up is recommended.