Open AccessAgenesis of female internal reproductive organs, the Mayer- Rokitansky-Küster-Hauser syndrome
Author(s) -
R. Sysak,
P. Bluska,
P Stencl,
M. Klein,
Ivan Varga
Publication year - 2021
Publication title -
bratislavské lekárske listy/bratislava medical journal
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.387
H-Index - 32
eISSN - 1336-0345
pISSN - 0006-9248
DOI - 10.4149/bll_2021_136
Subject(s) - mayer rokitansky kuster hauser syndrome , medicine , vagina , agenesis , gynecology , uterus , cervix , amenorrhea , surgery , obstetrics , pregnancy , cancer , biology , genetics
Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is the most common cause of uterine and uterine tubes absence/underdevelopment and the second most common cause of primary amenorrhea. It is characterized by a congenital agenesis of the uterine tubes, uterus, cervix, and upper part of the vagina. This study presents our 10 years of experience with the diagnostics and therapeutic management of patients with MRKH syndrome. We also focused on the description of anatomical deviations of the female reproductive organs.