Open AccessManagement of primary pulmonary alveolar proteinosis: A multicentric experience
Author(s) -
Vikas Marwah,
C.D.S. Katoch,
Sankalp Singh,
Ajay Handa,
Vasu Vardhan,
Ashok Kumar Rajput,
Madhusudan Barthwal,
D. Bhattacharyya
Publication year - 2020
Publication title -
lung india
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.457
H-Index - 25
eISSN - 0974-598X
pISSN - 0970-2113
DOI - 10.4103/lungindia.lungindia_401_19
Subject(s) - medicine , pulmonary alveolar proteinosis , hypoxemia , lung , respiratory system , pulmonary function testing , retrospective cohort study , biopsy , surgery
Pulmonary alveolar proteinosis (PAP) is a rare disease characterized by alveolar accumulation of surfactant material with reduced lung function and resulting hypoxemia. It is characterized by a variable clinical course, and whole lung lavage (WLL) is the standard treatment. Herein, we report our multicentric experience of management of primary PAP.