Open AccessMoyamoya disease presenting as alternating hemiparesis with relapsing remitting hemichorea: An unusual manifestation
Author(s) -
Siddharth Maheshwari,
Aldrin Anthony,
Suman Kushwaha,
Sandeep Singh,
Rupak Desai,
Dyutima Madan
Publication year - 2018
Publication title -
journal of pediatric neurosciences
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.247
H-Index - 18
eISSN - 1998-3948
pISSN - 1817-1745
DOI - 10.4103/jpn.jpn_85_18
Subject(s) - medicine , moyamoya disease , chorea , circle of willis , hemiparesis , differential diagnosis , movement disorders , presentation (obstetrics) , magnetic resonance imaging , internal carotid artery , stroke (engine) , pediatrics , radiology , disease , angiography , pathology , mechanical engineering , engineering
Moyamoya disease (MMD) is a neurological disease involving internal carotid artery (ICA) leading to its occlusion. Among the children, the disease presents as ischemic strokes, whereas in adults, it presents as hemorrhagic strokes. Movement disorder among the MMD is very rare with varied presentation. This article reports a case of 16-year-old girl presented with a history of alternating hemiparesis with recurrent hemichorea with self-remitting tendency. Magnetic resonance angiography brain showed marked-to-complete attenuation of supraclinoid ICA with multiple tortuous collateral vessels replacing the circle of Willis.