Open AccessHemiconvulsion-hemiplegia-epilepsy syndrome: A case series
Author(s) -
Harshit Bhargava,
Deepak Dwivedi
Publication year - 2020
Publication title -
journal of pediatric neurosciences
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.247
H-Index - 18
eISSN - 1998-3948
pISSN - 1817-1745
DOI - 10.4103/jpn.jpn_27_19
Subject(s) - medicine , epilepsy , status epilepticus , pediatrics , epilepsy syndromes , refractory (planetary science) , psychiatry , physics , astrobiology
Hemiconvulsion-hemiplegia-epilepsy (HHE) syndrome is an uncommon outcome of prolonged focal status epilepticus in childhood. We present four cases with age between 6 months and 3 years diagnosed with HHE syndrome. Two patients were lost to follow-up; other two cases had severe developmental delay and refractory epilepsy. An early diagnosis, a good seizure control, and a better understanding of the underlying mechanisms of HHE are needed to improve the outcome of this condition.