Open AccessCu-sil dentures: A novel approach of Papillon–Lefèvre syndrome management
Author(s) -
Shreya Tyagi,
Abi M Thomas,
Vinod Balla,
Ruchika Kundra
Publication year - 2019
Publication title -
journal of the indian society of pedodontics and preventive dentistry/journal of indian society of pedodontics and preventive dentistry
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.378
H-Index - 33
eISSN - 1998-3905
pISSN - 0970-4388
DOI - 10.4103/jisppd.jisppd_256_18
Subject(s) - dentures , medicine , girl , dermatology , dentistry , dentition , genetic disorder , cathepsin c , pediatrics , pathology , genetics , biology , cathepsin d , biochemistry , disease , enzyme
Papillon-Lefèvre syndrome (PLS) is a rare genetic disorder characterized by palmoplantar keratosis and premature loss of primary and permanent dentition. Its onset can be as early as 1-4 years of age. The genetic disorder is mutation in the cathepsin C gene. Hereby, we discuss the fabrication of Cu-sil dentures for the prosthetic rehabilitation of a 14-year-old girl with PLS. The case report describes the procedure and associated relevant information regarding the management protocols.