Cu-sil dentures: A novel approach of Papillon–Lefèvre syndrome management | Zendy

Shreya Tyagi | Zendy; Abi M. Thomas | Zendy; Vinod Balla | Zendy; Ruchika Kundra | Zendy

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Cu-sil dentures: A novel approach of Papillon–Lefèvre syndrome management

Author(s) -

Shreya Tyagi,

Abi M. Thomas,

Vinod Balla,

Ruchika Kundra

Publication year - 2019

Publication title -

journal of indian society of pedodontics and preventive dentistry

Language(s) - English

Resource type - Journals

SCImago Journal Rank - 0.378

H-Index - 33

eISSN - 1998-3905

pISSN - 0970-4388

DOI - 10.4103/jisppd.jisppd_256_18

Subject(s) - dentures , medicine , dermatology , genetic diagnosis , cathepsin c , girl , genetic disorder , dentistry , pediatrics , genetics , cathepsin d , gene , biology , biochemistry , disease , enzyme

Papillon-Lefèvre syndrome (PLS) is a rare genetic disorder characterized by palmoplantar keratosis and premature loss of primary and permanent dentition. Its onset can be as early as 1-4 years of age. The genetic disorder is mutation in the cathepsin C gene. Hereby, we discuss the fabrication of Cu-sil dentures for the prosthetic rehabilitation of a 14-year-old girl with PLS. The case report describes the procedure and associated relevant information regarding the management protocols.

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