Two cases of progressive familial intrahepatic cholestasis type 2: Role of surgery with brief review of literature | Zendy

KalyaniSaha Basu | Zendy; Hinglaj Saha | Zendy; Ghosh Tapanjyoti | Zendy; Somak Biswas | Zendy; PrafullaKumar Mishra | Zendy; Uttara Chatterjee | Zendy

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Two cases of progressive familial intrahepatic cholestasis type 2: Role of surgery with brief review of literature

Author(s) -

KalyaniSaha Basu,

Hinglaj Saha,

Ghosh Tapanjyoti,

Somak Biswas,

PrafullaKumar Mishra,

Uttara Chatterjee

Publication year - 2018

Publication title -

journal of indian association of pediatric surgeons

Language(s) - English

Resource type - Journals

SCImago Journal Rank - 0.306

H-Index - 17

eISSN - 1998-3891

pISSN - 0971-9261

DOI - 10.4103/jiaps.jiaps_235_17

Subject(s) - progressive familial intrahepatic cholestasis , medicine , cholestasis , gastroenterology , bile acid , intrahepatic bile ducts , liver transplantation , bile duct , transplantation

Progressive familial intrahepatic cholestasis (PFIC) is a rare bile acid transporter defect and autosomal recessive disorder with type 2 being the most common type. Partial internal or external biliary diversion delays its progression to end-stage liver disease. Here, we discuss two cases of type 2 PFIC.

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