Open AccessA rarer association of eosinophilic fasciitis
Author(s) -
U Namita,
S Rajesh,
C S Vidya
Publication year - 2019
Publication title -
journal of family medicine and primary care
Language(s) - English
Resource type - Journals
eISSN - 2278-7135
pISSN - 2249-4863
DOI - 10.4103/jfmpc.jfmpc_281_19
Subject(s) - medicine , eosinophilic fasciitis , fasciitis , etiology , dermatology , edema , pathogenesis , fascia , trunk , pathology , surgery , ecology , biology
Eosinophilic fasciitis (EF, also called Shulman syndrome) is a rare connective tissue disorder with poorly understood pathogenesis and unknown etiology. EF is characterized initially by limb or trunk erythema and edema and later by collagenous thickening of the subcutaneous fascia. Here, we present the case of a 16-year-old boy who presented with typical clinical features of EF with a history of typical trigger factor - preceding strenuous physical activity and had a rarer atypical association of hypercalcemia and raised angiotensin converting enzyme (ACE) levels.