Open AccessIdiopathic hypertrophic pachymeningitis as a rare cause of cervical compressive myelopathy
Author(s) -
Aya Fukuda,
Elizabete Punaro,
Fábio Rogério,
Luciano de Souza Queiróz,
Fabiano Reis
Publication year - 2017
Publication title -
journal of craniovertebral junction and spine
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.38
H-Index - 23
eISSN - 0976-9285
pISSN - 0974-8237
DOI - 10.4103/jcvjs.jcvjs_118_17
Subject(s) - medicine , myelopathy , spinal cord , spinal cord compression , magnetic resonance imaging , dura mater , pathology , mechanical compression , radiology , psychiatry , biomedical engineering
The spinal form of idiopathic hypertrophic pachymeningitis (IHP) is a rare condition characterized by a chronic progressive diffuse inflammatory fibrosis of the dura mater, which may evolve to the compression of the spinal cord. We present a case report about IHP focusing on its features in magnetic resonance imaging, which are determined by an intradural extramedullary mass in the cervical spine showing hypointensity on T2-weighted images and peripheral enhancement, causing compression of the spinal cord. Histological analysis showed a nonspecific chronic inflammatory process in dense fibrous tissue. The patient had a good outcome after therapy with steroids.