Open AccessIdiopathic Pulmonary Hemosiderosis in a Young Adult Patient: A Rare Case
Author(s) -
Abhishek Agarwal,
Rahul Kumar,
Anand Jaiswal,
Vikram Vohra,
Poulomi Chatterjee
Publication year - 2018
Publication title -
journal of association of chest physicians
Language(s) - English
Resource type - Journals
eISSN - 2320-9089
pISSN - 2320-8775
DOI - 10.4103/jacp.jacp_12_17
Subject(s) - medicine , diffuse alveolar hemorrhage , vasculitis , pathology , rare disease , hemosiderosis , purpura (gastropod) , granulomatosis with polyangiitis , microscopic polyangiitis , dermatology , disease , ecology , biology
Idiopathic pulmonary hemosiderosis (IPH) is often an ignored and rare cause of diffuse alveolar hemorrhage (DAH). It is characterized by triad of hemoptysis, anemia, and alveolar opacity on radiology. It is a diagnosis of exclusion, established after ruling out other causes of DAH such as Goodpasture’s syndrome, large vessel vasculitis, small vessel vasculitis associated with anti-neutrophil cytoplasmic antibody (ANCA) (Wegener’s granulomatosis, Churg–Strauss syndrome, microscopic polyangiitis), immune complex-related vasculitis (collagen vascular diseases, Henoch–Schönlein purpura, mixed cryoglobulinemia) drug reactions, anticoagulation and thrombocytopenia. Though it is a disease primarily affecting children, we hereby report a case of IPH in an adult patient who responded dramatically to oral corticosteroid