Open AccessRole of interventional radiology in the diagnosis and management of congenital extrahepatic portosystemic shunts: Two case reports
Author(s) -
Sheetal Vasundara Mathai,
Victor Kondray,
Elias Salloum,
Kamlesh Kukreja,
Sidhartha Tavri
Publication year - 2019
Publication title -
indian journal of radiology and imaging - new series/indian journal of radiology and imaging/indian journal of radiology and imaging
Language(s) - English
Resource type - Journals
eISSN - 0971-3026
pISSN - 0970-2016
DOI - 10.4103/ijri.ijri_461_18
Subject(s) - medicine , portosystemic shunt , asymptomatic , radiology , shunt (medical) , portal hypertension , occlusion , angiography , cirrhosis , portal venous pressure , portal venous system , surgery
Congenital extrahepatic portosystemic shunt (CEPS) is a rare splanchnic venous malformation, wherein the portal venous outflow drains into the systemic venous circulation via a pathologic shunt. CEPS exhibits heterogeneous clinical behavior and angiography is the gold standard for evaluation of the portomesenteric communication to systemic vasculature. The potential severity of complications necessitates shunt closure. Here, we present two cases of CEPS. The first patient presented with an asymptomatic hyperammonemia and was found to have a Type 1 CEPS with absence of intrahepatic portal system. The second patient was asymptomatic and was incidentally found to have a Type 2 CEPS on imaging with normal intrahepatic portal system. Both patients were successfully treated with endovascular occlusion of the CEPS.