Open AccessNon surgical management of unilateral lacrimal gland swelling in a paediatric patient of Rosai-Dorfman disease: A case report
Author(s) -
Sailie Shirodkar,
Prachi Patil,
Nagendra B. Shah
Publication year - 2019
Publication title -
indian journal of ophthalmology/indian journal of ophthalmology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 51
eISSN - 1998-3689
pISSN - 0301-4738
DOI - 10.4103/ijo.ijo_1596_18
Subject(s) - medicine , cervical lymphadenopathy , lacrimal gland , rosai–dorfman disease , cervical lymph nodes , biopsy , lymph node , work up , surgery , disease , radiology , pathology , cancer , metastasis
A 10-year-old girl presented to us with inferonasally displaced, non-axial proptosis of oculus dexter (OD), with ipsilateral, painless massive cervical lymphadenopathy of ten weeks duration. After a detailed hematological work-up and imaging, the histological evidence obtained on cervical lymph node biopsy established the diagnosis of Rosai-Dorfman disease. Although, Rosai-Dorfman disease of unilateral lacrimal gland is extremely infrequent, a high degree of suspicion is warranted in a case of young patient presenting with unilateral isolated lacrimal gland swelling and associated lymphadenopathy, wherein no other cause is found. Treatment protocol should be individualized as per the extent of systemic involvement and functional disability.