Open AccessA case of febrile ulceronecrotic Mucha-Habermann disease with comorbidities
Author(s) -
Dhanashree Bhide,
Mukta Shriram Tulpule,
Suresh V Pethe
Publication year - 2019
Publication title -
indian journal of dermatology, venereology, and leprology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.514
H-Index - 45
eISSN - 0973-3922
pISSN - 0378-6323
DOI - 10.4103/ijdvl.ijdvl_552_17
Subject(s) - malaise , medicine , dermatology , methotrexate , high fever , disease , diarrhea , surgery , pathology
Febrile ulceronecrotic Mucha-Habermann disease is a very rare and severe variant of pityriasis lichenoides et varioliformis acuta. Adult cases are difficult to diagnose as in the early course they can mimic erythema multiforme or lymphomatoid papulosis. We report a case of a 38-year-old woman who presented with 90% body surface area involvement, fever, diarrhea, malaise and associated comorbidities. She was treated with systemic steroids and methotrexate but suffered a fatal outcome. So far, a total of 65 cases are reported in the literature.