Open AccessIntracranial variant of encephalotrigeminal angiomatosis – A case report
Author(s) -
Niveditha Mohan,
R Karthik,
Saramma Mathew Fenn,
Pethagounder Thangavelu Ravikumar,
A Cicilia Subbulakshmi
Publication year - 2019
Publication title -
indian journal of dental research/indian journal of dental research
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.277
H-Index - 43
eISSN - 1998-3603
pISSN - 0970-9290
DOI - 10.4103/ijdr.ijdr_517_17
Subject(s) - angiomatosis , port wine stain , medicine , trigeminal nerve , population , bacillary angiomatosis , pathology , anatomy , laser , physics , environmental health , optics , bartonella henselae , serology , antibody , immunology
Encephalotrigeminal Angiomatosis is a rare developmental phakomatoses characterized by the occurrence of nevus flammeus (port-wine stain) along the distribution of branches of trigeminal nerve, vascular angiomas in the eye, and leptomeningeal angiomas affecting 1 in 1,00,000 South Asian population. Herewith, such a rare case of such encephalotrigeminal angiomatosis in a 24-year-old male is described.