Open AccessA fatal case of febrile ulceronecrotic mucha-habermann disease which presenting as toxic epidermal necrolysis
Author(s) -
Chen-jing Xing,
Hong Shen,
Jun Xu,
ZeHu Liu,
Junwu Zhu,
Aie Xu
Publication year - 2017
Publication title -
indian journal of dermatology/indian journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.395
H-Index - 36
eISSN - 1998-3611
pISSN - 0019-5154
DOI - 10.4103/ijd.ijd_631_16
Subject(s) - toxic epidermal necrolysis , medicine , etiology , dermatology , disease , mortality rate , pathology , surgery
Febrile ulceronecrotic Mucha-Habermann disease (FUMHD), a severe form of pityriasis lichenoides et varioliformis acuta, is an inflammatory dermatosis of unknown etiology manifested by ulcerative and necrotic lesions accompanied by systemic manifestations. The mortality rate of FUMHD is about 15%. It is reported here a case of FUMHD presenting as toxic epidermal necrolysis that resulted in multiple organ failure and death