Open AccessCraniotomy in Klippel-Trenaunay syndrome: Concerns and challenges
Author(s) -
R P Sangeetha,
Nisha Baskar,
Kamath Sriganesh,
Priyadharshi Dixit
Publication year - 2019
Publication title -
indian journal of anaesthesia/indian journal of anaesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.645
H-Index - 30
eISSN - 0976-2817
pISSN - 0019-5049
DOI - 10.4103/ija.ija_510_19
Subject(s) - medicine , klippel trenaunay syndrome , craniotomy , venous malformation , chiari malformation , surgery , congenital disorder , soft tissue , chiari i malformation , magnetic resonance imaging , radiology , syringomyelia
Klippel-Trenaunay syndrome (KTS) is a rare congenital disorder characterised by cutaneous capillary malformations, soft tissue and bone hypertrophy and venous varicosities. The coexistence of Chiari 1 malformation and an intracranial tumour has been rarely reported in the literature. Multisystem involvement of this syndrome mandates adequate preparation and planning, with meticulous conduct of anaesthesia to achieve favourable outcomes. We report a case of KTS syndrome with Chiari 1 malformation who had presented for craniotomy, and thereby discuss the challenges faced during anaesthetic management of these patients for major surgeries.