Open AccessAnesthetic management in a case of MURCS syndrome
Author(s) -
Poonam Arora,
JR Rekha,
RajnishKumar Arora,
Monica Arora
Publication year - 2021
Publication title -
al-banǧ. maqālāt wa abḥāṯ fī al-taẖdīr wa-al-in’āš
Language(s) - English
Resource type - Journals
ISSN - 0259-1162
DOI - 10.4103/aer.aer_137_21
Subject(s) - medicine , renal agenesis , anesthetic , presentation (obstetrics) , agenesis , hypoplasia , aplasia , surgery , dysplasia , poland syndrome , anesthesia , kidney
MURCS syndrome is a more severe form of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome, an acronym meaning aplasia/hypoplasia of Müllerian ducts (MU), congenital renal agenesis/ectopia (R), and cervical somite dysplasia (CS). A common presentation is primary amenorrhea in adolescent females. An anesthetist must consider the benefits and limitations of both regional and general anesthesia for these patients based on site of surgery and severity of malformations. We report successful anesthetic management of a 21-year-old female with MURCS syndrome scheduled for a creation of neovagina under spinal anesthesia using ultrasound guidance.