Open AccessA case report of mounier‑kuhn syndrome
Author(s) -
Keerthivasan Sivanmani
Publication year - 2017
Publication title -
journal of association of chest physicians
Language(s) - English
Resource type - Journals
eISSN - 2320-9089
pISSN - 2320-8775
DOI - 10.4103/2320-8775.196655
Subject(s) - bronchiectasis , medicine , abnormality , presentation (obstetrics) , atrophy , respiratory tract , disease , case presentation , lung , surgery , respiratory system , pathology , anatomy , psychiatry
Mounier-Kuhn syndrome is a congenital abnormality characterized by tracheobronchomegaly as a result of atrophy or absence of elastic fibers and thinning of smooth muscle layer in trachea and main bronchi. The usual presentation is one of recurrent respiratory tract infections with a broad spectrum of functional impairment ranging from minimal disease with preservation of lung function to severe disease in the form of bronchiectasis. We describe a case of an elderly man who presented with a recurrent respiratory infection who was subsequently diagnosed as Mounier-Kuhn syndrome