Open AccessPrimary pleural primitive neuroendocrine tumor: A rare entity
Author(s) -
Mayuri Johari,
Deepak Prajapat,
Arjun Khanna,
Deepak Talwar
Publication year - 2016
Publication title -
journal of association of chest physicians
Language(s) - English
Resource type - Journals
eISSN - 2320-9089
pISSN - 2320-8775
DOI - 10.4103/2320-8775.168623
Subject(s) - medicine , pleurodesis , pleural effusion , radiology , biopsy , lung , bronchoscopy , positron emission tomography , pathology
The rare primitive neuro-ectodermal tumors (PNET) are classically described as tumors of the airways that can metastasize to the pleura. We describe here, a rare case of a PNET originating from the pleura in a 52-year-old, nonsmoker female. The patient presented with clinical features of a right sided pleural effusion. Thoracoscopic pleural biopsy revealed malignant small round cell proliferation consistent with PNET, and the final diagnosis was confirmed by immune-histochemical analysis. Fiberoptic bronchoscopy, contrast enhanced computed tomography chest, and positron emission tomography scan did not reveal any primary lung lesion. The patient underwent pleurodesis for symptom relief but refused any definitive therapy