Open AccessDermatofibrosarcoma Protuberans: Insights into a Rare Soft Tissue Tumor
Author(s) -
Aliya Sarhan Al Barwani,
Sawsan Taif,
Reem Ahmed Al Mazrouai,
Khamis Salim Al Muzahmi,
Asif Alrawi
Publication year - 2016
Publication title -
journal of clinical imaging science
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.279
H-Index - 18
eISSN - 2156-7514
pISSN - 2156-5597
DOI - 10.4103/2156-7514.181492
Subject(s) - dermatofibrosarcoma protuberans , medicine , soft tissue , lesion , trunk , radiology , sarcoma , soft tissue sarcoma , hemangioma , presentation (obstetrics) , pathology , ecology , biology
Dermatofibrosarcoma protuberans (DFSP) is a rare soft tumor which originally represents a cutaneous sarcoma. It grows slowly and presents usually as nodular superficial lesion on the trunk or the extremities. Although these tumors are locally aggressive with high rate of recurrence following surgery; the prognosis is considered excellent when it is effectively treated. The radiological appearance of this tumor has rarely been studied and findings infrequently discussed in the literature probably because many lesions underwent resection before imaging. Although imaging is infrequently performed for this lesion; it can show characteristic features and demonstrate the full extent. Imaging may also play a role in the differentiation of this tumor from more serious soft tissue lesions such as more aggressive sarcomas and hemangioma. In this article, we discuss the imaging findings of DFSP that can aid in its diagnosis and its variable appearances. In addition; the clinical presentation and treatment options are also described with review of the previous literature