Castleman's Disease Presenting as Localized Abdominal Mass and Paraneoplastic Pemphigus
Author(s) -
Santosh Kumar,
Kshitij Bishnoi,
Pragatheeswarane Murugavaithianathan,
Vikas Kumar Panwar
Publication year - 2016
Publication title -
journal of clinical imaging science
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.279
H-Index - 18
eISSN - 2156-7514
pISSN - 2156-5597
DOI - 10.4103/2156-7514.177552
Subject(s) - paraneoplastic pemphigus , medicine , castleman disease , disease , pemphigus vulgaris , pemphigus , dermatology , pathology , lymphoproliferative disease , lymphoproliferative disorders , abdominal mass , systemic disease , lymphoma , autoantibody , immunology , antibody
Castleman′s disease is a rare, benign lymphoproliferative disorder of unknown origin. Paraneoplastic pemphigus is a common association which presents as oral mucosal ulcerations. Abdominal and retroperitoneal Castleman′s disease present either as a localized disease or as a systemic disease. We hereby present a 15-year-old male patient with oral mucosal lesions with localized vague right lower abdominal mass who was diagnosed to have Castleman′s disease with paraneoplastic pemphigus which was surgically excised
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