Open AccessLocalized Cystic Disease of the Kidney: A Rare Cause of Hypertension in a Young Adult
Author(s) -
Aynur Solak,
Mehmet Serkan Gür,
Berhan Genç,
Neslın Şahin
Publication year - 2013
Publication title -
journal of clinical imaging science
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.279
H-Index - 18
eISSN - 2156-7514
pISSN - 2156-5597
DOI - 10.4103/2156-7514.116191
Subject(s) - medicine , kidney , histopathology , kidney disease , renal function , autosomal dominant polycystic kidney disease , blood pressure , polycystic kidney disease , renal vein , disease , kidney disorder , cystic kidney disease , urology , outpatient clinic , pathology , surgery
Localized cystic disease of kidney (LCDK) is a rare, non-familial, non-progressive renal disorder that is not associated with cysts or disorders in other organs. Only a few cases have been reported in the literature. While this condition is morphologically identical to the autosomal dominant form of polycystic kidney disease, it is not inherited and is not associated with significant deterioration of renal function. We present a case of a 16-year-old male patient who suffered from hypertension for over two years. On imaging we found several, variable-sized cysts in the upper half of the right kidney. The left kidney and lower segment of the right kidney were normal. Selective renal vein catheterization and sampling showed markedly elevated renin level in the right upper segmental vein (92 pg/ml, normal value: 11-33 pg/ml). The patient underwent a right upper heminephrectomy and histopathology was suggestive of LCDK. After surgery, the patient′s blood pressure returned to normal levels without any need of antihypertensive medication and he is under follow-up on outpatient basis for the past two years