Open AccessAlveolar soft part sarcoma of the frontal calvarium and adjacent frontal lobe
Author(s) -
Kuntal Kanti Das,
Rohit Singh,
Sushila Jaiswal,
Vinita Agrawal,
Awadhesh Kumar Jaiswal,
Sanjay Behari
Publication year - 2012
Publication title -
journal of pediatric neurosciences
Language(s) - English
Resource type - Journals
eISSN - 1998-3948
pISSN - 1817-1745
DOI - 10.4103/1817-1745.97621
Subject(s) - medicine , alveolar soft part sarcoma , frontal lobe , sarcoma , frontal bone , soft tissue , metastasis , anatomy , pathology , skull , cancer , psychiatry
Alveolar soft part sarcoma is a rare tumor affecting mainly adolescent and young children. It presents as a slowly growing tumor and is usually overlooked due to lack of symptoms. Early metastasis is a characteristic feature of this tumor and, in a good number of cases, metastasis to the lung or brain is the first manifestation of the disease. In this report, we present a case of alveolar soft part sarcoma predominantly located in the right frontal bone with dural breach and contiguous right frontal lobe involvement in a 17-year-old girl without any evident primary or other secondaries. A brief review of literature is also presented.