Open AccessCardiac arrest after anesthetic management in a patient with hereditary sensory autonomic neuropathy type IV
Author(s) -
Yakup Ergül,
Barış Ekici,
Sabiha Keskin
Publication year - 2011
Publication title -
saudi journal of anaesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.416
H-Index - 24
eISSN - 1658-354X
pISSN - 0975-3125
DOI - 10.4103/1658-354x.76486
Subject(s) - medicine , anhidrosis , bradycardia , anesthesia , perioperative , autonomic neuropathy , anesthetic , surgery , heart rate , blood pressure , biology , genetics , cell culture , neuroblastoma
Hereditary sensory autonomic neuropathy type IV is a rare disorder with an autosomal recessive transmission and characterized by self-mutilation due to a lack in pain and heat sensation. Recurrent hyperpyrexia and anhydrosis are seen in patients as a result of a lack of sweat gland innervation. Self-mutilation and insensitivity to pain result in orthopedic complications and patients undergone recurrent surgical interventions with anesthesia. However, these patients are prone to perioperative complications such as hyperthermia, hypothermia, and cardiac complications like bradycardia and hypotension. We report a 5-year-old boy with hereditary sensory autonomic neuropathy type IV, developing hyperpyrexia and cardiac arrest after anesthesia.