Open AccessAnesthetic management of a patient with Bartter′s syndrome undergoing bilateral sagittal split osteotomy
Author(s) -
Nasser Nooh,
Walid Ahmed Abdullah,
Saad A. Sheta
Publication year - 2012
Publication title -
saudi journal of anaesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.416
H-Index - 24
eISSN - 1658-354X
pISSN - 0975-3125
DOI - 10.4103/1658-354x.105895
Subject(s) - medicine , bartter syndrome , bartter's syndrome , hyperaldosteronism , alkalosis , hypokalemia , metabolic alkalosis , muscle hypertrophy , pathophysiology , urology , surgery , aldosterone , acidosis
Bartter's syndrome is an unusual (estimated incidence is 1.2 per million people) but important congenital form of secondary hyperaldosteronism; due to abnormalities in renal handling of electrolytes. It is associated with hypertrophy and hyperplasia of the juxtaglomerular cells, normal blood pressure, and hypokalemic alkalosis withoutedema.We present a 22-year-old woman with Bartter's syndrome underwent bilateral sagittal split osteotomy to correct mandibular prognathic. The anesthetic management of Bartter's syndrome should be relevant to the pathophysiology of the syndrome. Therefore, it should be directed toward maintaining cardiovascular stability, control of associated fluid, electrolyte and acid-base derangements, and the prevention of renal damage.